ARUP's Laboratory Test Directory

Mucopolysaccharides, Quantitative, Urine : 0081357
[ image for: Patient History for Mucopolysaccharides (MPS) Testing]
Patient History for Mucopolysaccharides (MPS) Testing
[ image for: Additional Technical Information]
Additional Technical Information


Mnemonic: MPS QNT

Ordering Recommendation: Use to MONITOR glycosaminoglycans (GAGs) in patients previously diagnosed with a mucopolysaccharidosis (MPS). Approval by an ARUP genetic counselor or medical director required BEFORE ordering this test. To screen for MPS, refer to Mucopolysaccharides Screen - Electrophoresis & Quantitation, Urine (0081352).
Methodology: Spectrophotometry
Performed: Tue
Reported: 3-9 days
Specimen Required: Patient Prep: Morning void is preferred.

Collect: Urine.

Specimen Preparation: Transfer 10 mL urine to ARUP Standard Transport Tubes and freeze immediately. (Min: 5 mL)

Storage/Transport Temperature: Frozen.

Unacceptable Conditions: Contaminated specimens. Specimens containing preservatives.

Stability (collection to initiation of testing): Ambient: Unacceptable; Refrigerated: Unacceptable; Frozen: 1 month (avoid repeated freeze/thaw cycles)
Reference Interval:
0-5 months: 14.6-47.8 mg/mmol creatinine
6-11 months: 3.7-35.5 mg/mmol creatinine
1-2 years: 5.4-30.8 mg/mmol creatinine
3-6 years: 5.2-16.7 mg/mmol creatinine
7-13 years: 2.4-10.2 mg/mmol creatinine
14 years or older: 0.0-7.1 mg/mmol creatinine
Interpretive Data:

See Compliance Statement B: www.aruplab.com/CS
CPT Code(s): 83864
Cross References: GAG(s) (Mucopolysaccharides, Quantitative, Urine), Glycosaminoglycans (Mucopolysaccharides, Quantitative, Urine), Hunter (Mucopolysaccharides, Quantitative, Urine), Hurler (Mucopolysaccharides, Quantitative, Urine), Maroteaux-Lamy (Mucopolysaccharides, Quantitative, Urine), Morquio (Mucopolysaccharides, Quantitative, Urine), Sanfilippo (Mucopolysaccharides, Quantitative, Urine), Scheie (Mucopolysaccharides, Quantitative, Urine)